Li-11             DISEASES OF THE BILIARY SYSTEM              by Dr. E. Orfei


 

Contents

 

Normal biliary tract ( See li-2-3)

 

li-11-1 Bilirubin Metabolism and disorders.

 

li-11-2 Bile acids metabolism and disorders. 

 

li-11-3 Developmental defects

 

CYSTIC DISORDERS

-Simple non-parasitic cysts

-Congenital polycystic disease

DILATATIONS

-Congenital hepatic fibrosis

-Caroliís syndrome

 

ATRESIA

-Extrahepatic biliary atresia (EHBDA)

-Paucity of intrahepatic bile ducts, non syndromatic.

Byler's disease.

Noth american indian cholestasis.

Aagenaes syndrome (Hereditary cholestasis with lyphedema.)

- Paucity of intra-hepatic bile ducts, syndromatic.

Alagille syndrome

 

METABOLIC DEFECTS

Alpha-1-antitrypsin deficiency

Mucoviscidosis

Familial erythrophagocytic lymphohistiocytosis

li-11-4 Vanishing bile duct syndromes

IMMUNOLOGIC

Primary biliary cirrhosis.

Primary sclerosing cholangitis.

Graft versus host disease.

Hepatic allograft rejection.

Autoimmune cholangitis.

Sarcoidosis

TOXIC AND DRUG INDUCED

ISCHEMIC

INFECTIOUS

Bacterial.

Viral.

Protozoal.

NEOPLASTIC

Lymphoma.

Cholangiocarcinoma

Histiocytosis X

UNCLASSIFIED

Idiopathic adulthood ductopenia

li-11-5- Infections and infestations

Cholangitis, Cholangiolitis 

 

li-11-6- Drug and toxic lesions

li-11-7- Cholelithiasis

 

 

CONTENTS

-