Li-11          DISEASES OF THE BILIARY SYSTEM         by Dr. E. Orfei


 

 

Contents

 

li-11- Normal biliary tract ( See li-2-3 )


 

li-11-1-Bilirubin metabolism (Physiology and Pathology)


 

li-11-2-Bile acids metabolism (Physiology and Pathology)


 

li-11-3 Developmental disorders of Bile Ducts

CYSTIC DISORDERS

-Simple non-parasitic cysts

-Congenital polycystic disease

DILATATIONS

-Congenital hepatic fibrosis

-Caroliís syndrome

ATRESIA

-Extrahepatic biliary atresia (EHBDA)

-Paucity of intrahepatic bile ducts, non syndromatic( PIHBD)

Bylerís disease

North american indian cholestasis

Benign recurrent intrahepatic cholestasis

Metabolic defects

- Paucity of intra-hepatic bile ducts, syndromatic (SPIHBD)

Alagille syndrome

METABOLIC DIFECTS

Alpha-1-antitrypsin deficiency

Mucoviscidosis

Familial erythrophagocytic lymphohistiocytosis


 

li-11-4 Vanishing bile duct syndromes

IMMUNOLOGIC

-Primary biliary cirrhosis (PBC)

-Primary sclerosing cholangitis (PSC)

-Chronic graft -versus-host disease

-Hepatic allograft rejection

-Autoimmune cholangitis

-Sarcoidosis

TOXIC AND DRUG INDUCED

ISCHEMIC

INFECTIOUS

-Bacterial

-Viral

-Protozoal

NEOPLASTIC

-Lymphoma

-Cholangiocarcinama

-Histicytosis X

UNCLASSIFIED

-Idiopathic adulthood ductopenia

 


 

li-11-5- Infections and infestations

Cholangitis, Cholangiolitis


 

li-11-6- Drug and toxic lesions


 

li-11-7- Cholelithiasis


 

CONTENTS

 

 

 

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