Definition
Idiopathic pulmonary fibrosis is a pulmonary disease characterized by interstitial fibrosis of unknown etiology.

Pathology

Etiology/Pathogenesis
Unknown. In actually this pathologic condition may be the end stage of manydifferent pulmonary diseases.

Pathophysiology
Hypoxemia, dyspnea, cyanosis, pulmonary hypertension and cor pulmonale.