Idiopathic pulmonary fibrosis is a pulmonary
disease characterized by interstitial fibrosis of
- The pathology, which is non-specific, varies with the stage of the disease.
- The dominant pattern is inflammatory early on leading to
organization of the exudate and interstitial fibrosis in the later stage.
- The severe septal thickening (fibrosis) leads to a "honeycomb"
appearance of the lung and pronounced alveolocapillary block. Refer to
Figure 15-35 in your textbook.
Unknown. In actually this pathologic condition may be the end stage of manydifferent
Hypoxemia, dyspnea, cyanosis, pulmonary hypertension and cor pulmonale.